The palate is generally formed at around 8-10 weeks gestation, when the two shelves of the palate grow and join at the midline forming the “roof of the mouth”. The high position of the tongue then interferes with the closure of the palate. As a result the tongue sits high and is pushed backwards into the airway. The underdeveloped jaw causes the tongue to become crowded within the mouth. In a child with PRS, this growth is restricted, resulting in the lower jaw being much smaller than it’s expected size. In the absence of a cleft a highly arched palate may occur.ĭuring the very early stages of pregnancy, a foetus jaw goes through a rapid growth period. Although a cleft palate usually occurs in PRS, a cleft is not a necessary feature for diagnosis. The existence of all three abnormalities together determines the diagnosis of Pierre Robin Sequence. upper respiratory breathing obstruction.a tongue that is further back than usual ("glossoptosis").a small or underdeveloped lower jaw (“micrognathia” pronounced micro-nath-ea).Pierre Robin (Pronounced Row-barn) Sequence (PRS) is a condition characterised by the existence of three abnormalities:
The following information aims to provide valuable and meaningful information about PRS. Information for the condition is varied and conflicting. It is referred to by various names including:
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